Rehabilitation Practice and Science
Translated Title
復健治療對一位十一歲女童罹患戴維克症候群之臨床療效:病例報告
Abstract
Devic's syndrome-neuromyelitis optica (NMO), a rare demyelinating central nervous system diseases, must be clinically differentiated from multiple sclerosis (MS). The diagnostic criteria of Devic's syndrome include optic neuritis, acute myelitis, and at least two of the three symptoms below: brain MRI different from MS, three or more consecutive spinal segments invaded on MRI, and NMO-IgG seropositive.The case prevails over females aged 30-40 years. The courses of Devic's syndrome could be categorized in two types: single invasion and recurrence. The latter has poorer prognosis. The medical treatment mainly lies in immune modulation and the rehabilitative intervention including retaining life functions, preventing complications, and ameliorating life quality. We report a rare case that the eleven-year-old girl suffered from acute loss of visual acuity at the age of 6 attributed to optic neuritis of unknown origin. After high dose steroid prescription, no significant improvement was noted. Additionally, Devic's syndrome was diagnosed under: the repeated attacks of acute myelitis within two years, optic neuritis, acute myelitis invading more than three consecutive spinal segments, and NMO-IgG seropositive. The immunosuppressive therapy and the 3-day-a-week rehabilitation programs were offered. Subsequently, the scale result of the Wee Functional Independence Measure scale rose massively; the complications such as fatigue, spasm, muscle strength loss, and neurogenic bladder dysfunction) were prevented. Although, the recurrent course led to the functional deterioration, the rehabilitation training maintained the maximum functional independence of life.
Language
Traditional Chinese
DOI Link
https://doi.org/10.6315/2010.38(1)06
First Page
41
Last Page
47
Recommended Citation
Hsu, Cheng-Cheng; Lin, Wen-Chih; Lau, Tan-Hwui; Lai, Ming-Chi; Hong, Rong-Bin; and Chou, Wei-Ni
(2010)
"Clinical Outcomes of Rehabilitation on an 11-year-old Girl with Devic's Syndrome: A casereport,"
Rehabilitation Practice and Science: Vol. 38:
Iss.
1, Article 6.
DOI: https://doi.org/10.6315/2010.38(1)06
Available at:
https://rps.researchcommons.org/journal/vol38/iss1/6