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Rehabilitation Practice and Science

Translated Title

裘馨氏肌肉失養症患者呼吸狀況的偵測

Abstract

The life expectancy of individuals with untreated Duchenne muscular dystrophy(DMD) is around 18-19 years. The cause of their death is mostly from respiratory complications. Early detection of respiratory function will provide the opportunity of early management and prolong their life span.This study included 30 patients with DMD in a period of three years and took a cross-section design. All the data were obtained by telephone interview with the patients or their family. Nineteen of 30 patients accepted functional evaluation in Brooke’s grading scale and pulmonary function test(PFT). Ten of these 19 patients received nocturnal breathing monitor including O2 saturation and end-tidal CO2.. The result showed that 8 of 19(42%) patients who received PFT had impaired respiratory function. all the patients with impaired pulmonary function lost their ambulation ability simultaneously. Four of 10 patients(40%) with nocturnal breathing monitor had nocturnal oxygen desaturation (NOD). The patients whose vital capacity below 50% of prediction got a more chance to develop NOD, but there was no significant difference in statistics. It is suggested that DMD patients should have a routine pulmonary function test once they progressively lost their ambulation ability. Nocturnal breathing monitor should be performed in DMD patients when their vital capacity was below 50% of predicted value for early detection of NOD and early management.

Language

Traditional Chinese

First Page

97

Last Page

104

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