Comparing findings of Hemophilia Joint Health Score and Hemophilia Early Arthropathy Detection with Ultrasound assessments in Taiwanese patients with severe hemophilia

Authors

Yen-Ling Huang, Department of Physical Medicine and Rehabilitation, Chung Shan Medical University Hospital, Taichung 40201, Taiwan
Hong-Yi Lin, Department of Physical Medicine and Rehabilitation, Chung Shan Medical University Hospital, Taichung 40201, Taiwan
Te-Fu Weng, Department of Pediatrics, Chung Shan Medical University Hospital, Taichung 40201, Taiwan
Sheng-Wei Zeng, Department of Rehabilitation, Tung Wah Hospital, Nantou City 557, Taiwan
Yueh-Han Ku, Department of Physical Medicine and Rehabilitation, Chung Shan Medical University Hospital, Taichung 40201, Taiwan
Yu-Hui Huang, Department of Physical Medicine and Rehabilitation, Chung Shan Medical University Hospital, Taichung 40201, TaiwanFollow

Abstract

Purpose: This study aimed to evaluate the correlation between Hemophilia Joint Health Score 2.1 (HJHS 2.1) and Hemophilia Early Arthropathy Detection with Ultrasound (HEAD-US) in Taiwanese patients with severe hemophilia and identify specific items within HJHS to predict early ultrasonic changes in hemophilic arthropathy (HA).

Methods: Thirty-six patients with a total of 210 joints were evaluated. We used Spearman's rank correlation coefficient to analyze the correlation between these two scales. The sensitivity, specificity, and accuracy of each HJHS item were also calculated to predict early HA.

Results:These two scales showed very strong correlation in the total scores (r = 0.84, p < 0.01) and moderate strong correlation in subtotal scores of elbow, ankle and knee joints (r=0.67, 0.57, 0.78 accordingly, all p

Conclusion: The correlation between the two scales is strong in severe hemophilic patients. Limited range of motion in the three joints indicates the need for further image evaluation.

Recommended Citation

Huang, Yen-Ling; Lin, Hong-Yi; Weng, Te-Fu; Zeng, Sheng-Wei; Ku, Yueh-Han; and Huang, Yu-Hui (2024) "Comparing findings of Hemophilia Joint Health Score and Hemophilia Early Arthropathy Detection with Ultrasound assessments in Taiwanese patients with severe hemophilia," Rehabilitation Practice and Science: Vol. 2025: Iss. 1, Article 6.
DOI: https://doi.org/10.6315/3005-3846.2249
Available at: https://rps.researchcommons.org/journal/vol2025/iss1/6