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Rehabilitation Practice and Science

Translated Title

脊髓性肌肉萎縮症吞嚥障礙的處理

Abstract

Spinal muscular atrophy (SMA) is an autosomal recessive neuromuscular disease. SMA phenotypes can be determined by the timing of disease onset and the highest level of motor development reachable by the patient. Generally speaking, proximal muscle involvement is more severe than in the distal extremities. In addition, cervical and the masticatory and pharyngeal muscles were likely affected by the disease, which can cause feeding problems and dysphagia. Clinically, dysphagia is more common among patients with type I and type II SMA. To thoroughly evaluate swallowing-related issues, both subjective information from patients and their caregivers and findings from objective tools including video fluoroscopic swallowing studies and fiber-optic endoscopic swallowing evaluations are required. Based on the results of the comprehensive swallowing assessment, further management including food content adjustment, swallowing training and tube feeding can be implemented. The aim of this reviewarticle is to present the current available information and evidence regarding the clinical presentation, assessment, and management of dysphagia in SMA patients.

Language

Traditional Chinese

First Page

11

Last Page

16

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