Moyamoya Disease Presenting with Hemichorea: A casereport

Authors

Min-Hsin Lai
Shin-Yo Lu
Pei-Chi Chou
Shin-Tsu Chang
Heng-Yi Chu

Translated Title

以舞蹈症爲表現的毛毛樣腦血管病變：病例報告

Abstract

We report an unusual case of a 13-year-old boy with moyamoya disease whose predominant manifestation was right hemichorea with initial dystonic spasms of the right limbs and face. A diffusion-weighted MR image of the brain in the initial stage showed no infarcted or other parenchymal lesions. However, MR angiography and intracranial angiography showed stenosis of the bilateral internal carotid and middle cerebral artery with prominent basal collaterals, which was compatible with moyamoya disease. Chorea or hemichorea is one of the rarer presenting features of moyamoya disease. Our findings suggest that moyamoya disease should be included in the differential diagnosis of pediatric onset chorea.

Language

English

DOI Link

https://doi.org/10.6315/2010.38(3)04

First Page

169

Last Page

174

Recommended Citation

Lai, Min-Hsin; Lu, Shin-Yo; Chou, Pei-Chi; Chang, Shin-Tsu; and Chu, Heng-Yi (2010) "Moyamoya Disease Presenting with Hemichorea: A casereport," Rehabilitation Practice and Science: Vol. 38: Iss. 3, Article 4.
DOI: https://doi.org/10.6315/2010.38(3)04
Available at: https://rps.researchcommons.org/journal/vol38/iss3/4