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Rehabilitation Practice and Science

Translated Title

兒童小腦動靜脈畸形出血後之小腦性緘默症:兩病例報告

Abstract

Cerebellar mutism syndrome is a rare but devastating consequence following posterior fossa surgery or lesion. It tends to occure predominantly in children, and is characterized by transient mutism, oromotor apraxia, apathy, hypokinesis, irritability and mood lability. The vermis, paravermian region and deep cerebellar nuclei are important structures which are highly correlated with the occurrence of cerebellar mutism syndrome. We report two cases, aged 11 and 15 years, who developed cerebellar mutism after rupture of posterior fossa arteriovenous malformation. Swallowing difficulty, irritability and aggressive behavior occurred concomitant with mutism. For the two cases, their symptoms of mutism lasted for 6 months and 2.5 months respectively. Unfortunately, dysarthria occurred following the resolution of mutism, even though the swallowing ability and behavioral control improved. The pathophysiologic mechanism of this syndrome may be due to crossed cerebello-cerebral diaschisis caused by tissue swelling, vasospasm or direct injury to these structures of cerebellum. The long term effect of cerebellar mutism on high cognitive function remains to be investigated.

Language

Traditional Chinese

First Page

117

Last Page

124

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